Hernia Uterine Inguinale (Uterine Hernia Syndrome). Individuals with this syndrome appear to be normal males, but relatively well-differentiated mullerian duct structures are found, usually a uterus and tubes in an inguinal hernia sac. This is due to a failureure of AMH function either as a result of failureure of Sertoli cell secretion of this polypeptide or an inability of the mullerian ducts to respond to AMH. It is inherited as a recessive trait, either X-linked or autosomal. Fertility is usually preserved. Other instances in which some mullerian duct retention is found include dysgenetic testes, ovotestes, mixed gonadal dysgenesis, mullerian duct and utricular cysts, and prenatal diethylstilbestrol (DES) exposure.